Spine Surgeons conducting a Cervical spine procedure

SPLIT SPINAL CORD MALFORMATION

Split spinal malformation, also known as diastematomyelia, refers to a rare congenital condition. At birth the child will have a split spinal cord, instead of being a single unified structure.  The spinal cord will appear divided longitudinally by a bony, fibrous, or even cartilaginous spur. This “split” can appear complete, forming two separate hemicords.

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3 percent of individuals with progressive curvature may eventually experience severe problems that can include scoliosis and back pain, spinal problems, and nerve compression causing numbness, weakness, and leg pain.

Split Spinal Cord Malformation

Split spinal cord malformationSplit spinal cord malformation, also known as diastematomyelia, refers to a congenital condition that affects the spinal cord’s normal development. This complex malformation involves the division of the spinal cord into two separate parts, each encased in its protective covering. In this comprehensive document, we will delve into the definition, causes, symptoms, diagnosis, and various treatment approaches for split spinal cord malformation. Additionally, we will explore the benefits of surgical treatment, the recovery period, and reasons why patients might consider seeking care at the Southwest Scoliosis and Spine Institute.

Split spinal cord malformation appears as a congenital anomaly characterized by the division of the spinal cord into two distinct parts. This occurs due to incomplete fusion of the neural tube during embryonic development, leading to the formation of two separate spinal cord segments. The condition may manifest along the length of the spinal column, potentially causing various neurological and orthopedic issues.

Split Spinal Cord Malformation Causes:

The primary cause of split spinal cord malformation lies in disruptions during the early stages of fetal development. Doctors associate this condition with an incomplete closure of the neural tube, a crucial structure that forms the foundation of the central nervous system. Genetic factors and environmental influences may contribute to the occurrence of this congenital malformation.

Questions and Answers

What is Split Spinal Cord Malformation (SSCM)?

SSCM, also known as diplomyelia, refers to a congenital spinal anomaly where the spinal cord becomes divided into two distinct hemicords.  Specifically, this condition occurs during fetal development and can lead to neurological issues. Because the split spinal cord may appear complete or incomplete, the severity of symptoms can vary.

What Symptoms Are Associated with Split Spinal Cord Malformation?

Symptoms of SSCM can include motor and sensory deficits, abnormal reflexes, and musculoskeletal issues. Also, the specific symptoms depend on the location and extent of the split.  Furthermore, individuals may experience problems with coordination, strength, and sensation in the affected areas. Additionally, some cases may be asymptomatic, while others can lead to significant neurological challenges.

How is Split Spinal Cord Malformation Treated?
 
Treatment for SSCM depends on the severity of symptoms and associated complications. In some cases, conservative management, such as physical therapy, pain management, and monitoring for potential issues, can work well. However, doctors may recommend surgical intervention in cases where there is a risk of worsening neurological function or if there are associated abnormalities that require correction. The goal of surgery is to address the anatomical abnormalities and improve overall spinal cord function.
 
 
 

Symptoms:

The symptoms of split spinal cord malformation can vary widely, and their severity depends on the extent of the malformation. Common symptoms include:

  • Back Pain: Pain in the back or spine.
  • Neurological Symptoms: Such as muscle weakness, numbness, or tingling in the lower extremities.
  • Orthopedic Issues: Deformities of the spine, such as scoliosis or kyphosis.
  • Bladder and Bowel Dysfunction: In some cases, problems with urinary or bowel control may occur.

Diagnosis:

Diagnosing split spinal cord malformation involves a comprehensive approach that combines the following techniques:

  • Medical History: Physicians often conduct a detailed assessment of the patient’s symptoms and medical history.
  • Physical Examination:
  • Imaging Studies: MRI or CT scans to visualize the spinal cord and identify the presence of a split or divided cord
  • Electromyography (EMG) and Nerve Conduction Studies: To assess nerve function and identify any abnormalities.

Treatment Methods:

The treatment of split spinal cord malformation is typically individualized based on the severity of symptoms and associated issues. Treatment may include:

  • Observation: In cases where symptoms appear mild and do not cause significant impairment, doctors may implement a watch-and-wait approach.
  • Physical Therapy: Exercises to improve muscle strength, flexibility, and overall function.
  • Orthopedic Management: Doctors may recommend bracing or other orthopedic interventions to address spinal deformities.
  • Surgery: In severe cases with significant symptoms or complications, doctors may recommend surgical intervention.

Surgical Procedures:

There are several surgical procedures aimed at addressing the complexities of split spinal cord malformation.

  • Detethering Surgery: One common surgical procedure is detethering surgery, which aims to release any abnormal attachments of the spinal cord to surrounding tissues. This procedure is particularly crucial when a tethered spinal cord is present, as it helps alleviate tension and prevent further complications.
  • Spinal Fusion: Doctors use spinal fusion as another surgical option. This procedure involves joining two or more vertebrae together, stabilizing the spine, and preventing further misalignment. Spinal instrumentation, such as rods, screws, or other devices, will support and maintain spinal alignment. In cases of associated scoliosis or other spinal deformities, doctors may use spinal fusion to stabilize the spine.
  • Tumor Excision: In cases where associated tumors appear present, doctors may use surgical excision to remove them. This not only addresses the tumor but also helps alleviate pressure on the spinal cord.

Non-Surgical Treatment:

In cases where symptoms appear mild and do not cause significant impairment, our doctors will first take a conservative approach. This can involve close observation and monitoring of the condition. Physical therapy plays a pivotal role in managing split spinal cord malformation. Tailored exercises will improve muscle strength, flexibility, and overall functional ability. Orthopedic management, including the use of braces or other interventions, works well to address spinal deformities and provide support.

Benefits of Surgical Treatment:

Surgical treatment for split spinal cord malformation offers several benefits, including the potential for improved neurological function, stabilization of the spine, and prevention of further deformities. Detethering surgery can release tension in the spinal cord, reducing the risk of complications such as neurological deficits. In addition, spinal fusion and instrumentation provide structural support, contributing to enhanced spinal stability and alignment.

Additionally, surgical intervention may alleviate pain and improve the patient’s overall quality of life. Furthermore, the benefits extend beyond the physical realm, positively impacting psychological well-being and functional independence.

Recovery Period:

The recovery period following surgical treatment for split spinal cord malformation varies depending on the specific procedures performed and the individual patient’s response. In general, patients may experience a period of postoperative care, including pain management, physical therapy, and close monitoring for any signs of complications.

Physical therapy plays a crucial role in the recovery process. Moreover, therapists work closely with patients to gradually regain strength, flexibility, and functional abilities. The duration of the recovery period can range from weeks to months, and ongoing follow-up appointments with healthcare providers are essential to monitor progress and address any concerns.

Reasons to Choose the Southwest Scoliosis and Spine Institute:

Patients facing the complexities of split spinal cord malformation should seek treatment at the Southwest Scoliosis and Spine Institute. This specialized institute offers several advantages:

  • Experienced Specialists: The institute is staffed with experienced spine specialists who possess expertise in the diagnosis and treatment of complex spinal conditions, including split spinal cord malformation.
  • Comprehensive Diagnostic and Treatment Options: The institute provides a range of comprehensive diagnostic and treatment options, ensuring that each patient receives individualized care tailored to their unique needs.
  • Multidisciplinary Approach: The Southwest Scoliosis and Spine Institute employs a multidisciplinary approach, involving collaboration among various healthcare professionals to address the diverse aspects of spinal conditions.
  • Focus on Individualized Care: Patients benefit from a patient-centered approach, where treatment plans are customized to address their specific symptoms, concerns, and goals.
  • Advanced Surgical Techniques: The institute maintains state-of-the-art technology, allowing for precision in surgical interventions and enhancing overall treatment outcomes.

Conclusion

In conclusion, the treatment of split spinal cord malformation necessitates a thorough understanding of its condition. While non-surgical treatments may suffice in milder cases, surgical interventions offer significant benefits in managing severe symptoms and preventing further complications. Therefore, the decision to choose surgical treatment is guided by individualized considerations, and the recovery period involves emphasizing physical therapy and postoperative care. For patients seeking specialized care for split spinal cord malformation, they should consider the Southwest Scoliosis and Spine Institute with offices in Dallas, Plano, and Frisco, Texas.  The reason is simple — we are a reputable and comprehensive center offering experienced specialists, individualized care, and advanced treatment options.

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National Library of Medicine: Characteristics of Split Spinal Cord Malformation

 

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